腫瘤相關(guān)低磷骨軟化癥掌骨溶解:1例報(bào)告和綜述
摘要: 腫瘤相關(guān)性低磷骨軟化癥(tumor-induced osteomalacia, TIO)是一種罕見疾病,磷酸鹽尿間質(zhì)腫瘤(phosphaturic mesenchymal tumor, PMT)是大多數(shù)TIO患者的病理基礎(chǔ),PMT會(huì)異常過量分泌成纖維細(xì)胞生長因子23 (fibroblast growth factor23, FGF-23),導(dǎo)致腎臟磷酸鹽異常消耗,引發(fā)血磷下降、... ...
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